L-Phenylalanine CAS: 63-91-2 99% ọcha ntụ ntụ
Nọmba katalọgụ | XD90317 |
Aha ngwaahịa | L-Cysteine hydrochloride anhydrous |
CAS | 63-91-2 |
Usoro ihe omimi | C9H11NO2 |
Ibu molekụla | 165.19 |
Nkọwa nchekwa | Ambient |
Koodu tarifu akwadoro | 29224985 |
Nkọwapụta ngwaahịa
Ọdịdị | White crystalline ntụ ntụ |
Nyocha | 99% |
Ntughari pụrụ iche | -20.4 ruo -35.2 |
Ọla dị arọ | <0.002% |
Ndu | <10mg/kg |
pH | 5.4-6 |
Ọnwụ na ihicha | <0.40% |
Ihe fọdụrụ na mgbanye | <0.10% |
Na ọrịa maple sirop (MSUD), branched-chain L-amino (BCAA) na 2-oxo acid (BCOA) na-agbakọta n'ime mmiri anụ ahụ n'ihi ụkọ ketara eketa nke alaka-chain 2-oxo acid dehydrogenase complexer.Na MSUD, ntakịrị ozi dị na mkpa mkpofu mmamiri nke ogige ndị nwere alaka.Anyị nyochara mkpochapụ gbasara akụrụ nke leucine, valine, isoleucine na alloisoleucine, yana 2-oxo acids 4-methyl-2-oxopentanoate (KIC), 3-methyl-2-oxobutanoate (KIV), (S) - (S- KMV), na (R) -3-methyl-2-oxopentanoate (R-KMV), na-eji ụzọ abụọ nke plasma na urine sample (n = 63) sitere na ndị ọrịa 10 nwere MSUD oge gboo.Mpụpụ gbasara akụrụ nke BCAA n'efu nọ n'ogo nkịtị (<0.5%) ma na-adabereghị na mkpokọta plasma.Mpụpụ nke bound (N-acylated) BCAA bụ ihe nkịtị ma ọ dabereghị nke ukwuu na mkpokọta plasma BCAA.Mpụpụ gbasara akụrụ nke BCOA dị n'usoro KIC << KIV